Osteogenesis imperfecta in adults: a challenge in anesthetic management

Main Article Content

Edwin Monar
Fabiola Lira

Abstract

Osteogenesis Imperfecta (OI) prevalence is estimated at between 1/10000 and 1/20000.
It is an autosomal dominant disorder associated with mutations in collagen type I genes. OI survival
estimation depends of its severity grade; hence there are cases that reach to adulthood. This is a successful
case report of appropriate Anesthetic Management which was complex due to airway access difficulties.
The methodology used involved Video Stylet (VS) intubation and Total Intravenous Anesthesia (TIVA)
avoiding the use of medication that might cause secondary effects such as: malignant hyperthermia and
restrictive pulmonary disease.

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How to Cite
1.
Monar E, Lira F. Osteogenesis imperfecta in adults: a challenge in anesthetic management. REMCB [Internet]. 2019May30 [cited 2024Jul.3];40(1):59-3. Available from: https://remcb-puce.edu.ec/remcb/article/view/784
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Notas científicas

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